STRATEGIES FOR ORAL CARE IN PATIENTS WITH EPIDERMOLYSIS BULLOSA

Abstract

Introduction. Rare (orphan) diseases are traditionally defined as diseases that affect very few people but can be associated with inadequate treatment, chronic exhaustion, and adverse health outcomes. One of the most severe hereditary dermatoses is epidermolysis bullosa (EB). In addition to skin lesions, depending on the form of EB, it has pronounced symptoms in the oral cavity. The development and progression of these symptoms are influenced not only by general factors but also by local factors, primarily poor oral hygiene due to the formation of blisters in and around the oral cavity, scarring contractures around the mouth, microstomia, reduced tongue mobility, and insufficient hand motor skills. The aim of the study. Based on personal research and analysis of literature sources, to systematize recommendations for oral care in patients with epidermolysis bullosa. Research materials and methods. Two clinical cases of patients with the dystrophic form of EB are presented. In one case, the diagnosis of “Exacerbation of chronic granulating periodontitis was established”; in the other, “Chronic fibrous pulpitis”. After achieving a satisfactory degree of mouth opening (clinical case № 1 – myogymnastics, clinical case № 2 – surgical intervention), treatment was carried out for the exacerbation of chronic granulating periodontitis of tooth 23 (clinical case № 1) and the extraction of teeth 41, 42, 43, 44 (clinical case № 2). Results. As a result of personal research and analysis of literature sources, recommendations for oral care were systematized, aimed at preventing the development of pathological changes in the oral cavity. Conclusions. Oral care is an effective and necessary element of the prevention of dental diseases in patients with EB, as it helps not only to prevent the development of pathological changes in the oral cavity but also to improve the general well-being and quality of life of such patients.